Prognostic factors in cutaneous T-cell lymphoma

R Willemze

doi:10.4081/hmr.v3i1.550

Abstracts

11 June 2009

Vol. 3 No. 1 (2009)

https://doi.org/10.4081/hmr.v3i1.550

Prognostic factors in cutaneous T-cell lymphoma

Publisher's note
All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.

PDF

250

Views

1564

Downloads

Authors

R Willemze

support@pagepress.org

Cutaneous T-cell lymphoma (CTCL) are a heterogeneous group of neoplasms of skin-homing T cells that show considerable variation in clinical presentation, histological appearance, immunophenotype and prognosis. In recent classification schemes (WHO-EORTC; WHO 2008) roughly three categories of CTCL can be distinguished: (1) the group of classical CTCL, including mycosis fungoides (MF, variants or subtypes of MF (folliculotropic MF; pagetoid reticulosis; granulomatous slack skin) and Sézary’s syndrome (SS); (2) the group of primary cutaneous CD30-positive lymphoproliferative disorders (CD30+ LPD); and (3) a group of rare often aggressive cutaneous T/NK cell lymphomas, including subcutaneous panniculitis-like T-cell lymphoma (SPTCL), extranodal NK/T-cell lymphoma, nasal type, and primary cutaneous peripheral T-cell lymphoma, not otherwise specified (PTL, NOS) as well as some rare subtypes of PTL, NOS.1,2